摘要：目的 总结成人法乐四联症根治术的外科治疗经验.方法 对2007年6月至2009年8月收治的22例18岁以上成年法乐四联症患者进行手术根治.所有病例均经右室切口疏通右室流出道(RVOT),同时修补室间隔缺损.跨瓣环RVOT补片13例,单纯RVOT补片6例,肺动脉与RVOT分别予以补片1例.结果 术后室间隔残余分流2例,重度低心排1例,经抢救无效死亡,病死率4.55%.结论 根据成人法乐四联症特点,合理设计手术方案,成人法乐四联症根治术可取得良好效果. Abstract： Objective To summarize the experience of radical treatment of tetralogy of Fallot in adults. Methods Between June 2007 and August 2009, 22 patients over 18 years old with tetralogy of Fallot underwent total surgical correction.Longitudinal or oblique right ventriculotomy was used to ensure complete release of right ventricular outflow obstruction and complete ventricular septal defect closure. Transannular patches were used in 13 cases, right ventricular outflow tract(RVOT)patches in 6 cases. Both pulmonary artery and right ventricular outflow tract(RVOT)patches in 1 case. Results Two cases had residual ventricular shunt, one case died of low cardiac output syndrome with a fatality of 4.55%. Conclusions By careful surgical management, total correction of tetralogy of Fallot in adult patients may results in good effects.

关键词：成人 法乐四联症根治术 外科治疗 tetralogy of 

单位：郑州大学第一附属医院心血管外科 450052 河南省人民医院心血管外科